3. Hirschsprung’s Disease
• It is a form of chronic intestinal
obstruction caused by congenital
absence of ganglion cells in both the
intermuscular and submucosal
plexuses.
5. Extent of Aganglionosis
• Short segment (75%):
Rectosigmoid.
• Long segment (20%):
Descending colon.
• Total Colonic (5%):
Colon and parts of
small intestine.
6. Clinical Picture
• Age: 50% neonates,
45% up to 2 yrs,
5% > 2yrs.
• Failure to pass
meconium within
48hrs
• Abdominal
distension.
• Constipation.
10. Surgical Treatment For
Hirschsprung’s Disease
• Three Stages: Outdated.
• Two Stages: Standard (colostomy, pull through).
• One Stage: Selected cases.
11. Age for definitive Pull through
• 9 months: Out dated.
• 6 months: Standard.
• Neonates: Selected cases.
12. Type of Surgery
• Abdomino-perineal pull through.
• Trans anal pull through.
19. ASSOCIATED DEFECTS
Urogenital
- Most common
- 20 – 45 %
- The higher the malformation the higher the incidence
Sacrum and Spine
- Sacrum frequently abnormal deformed
reduced in number
hemisacrum
- Spine frequently shows hemivertebrae
20. D.D: Functional (Constitutional)
Constipation.
• Common complaint: Constipation or
incontinence.
• History: Period of normal defecation
followed by constipation.
• Age: from infancy to puberty.
• Causes: Emotional & stress, chronic
dehydration, anal fissure, drugs (opiates &
anticholinergic), hypothyroidism.
26. CONCLUSION
• Early detection, proper diagnosis &
management of constipation in
children gives excellent results.
• Hirschsprung’s disease should be
suspected in cases of constipation
resisting ordinary treatment.