One of lectures presented in our Port said fifth neonatology conference, 23-24 October 2014 by Prof Mohamed El Sawy, Prof in Pediatric department , faculty of medicine, Ain Shams university

1. بسم ال الرحمن الرحيم

2. INTERSEX
By
Mohamed El-Sawy
Prof. in Pediatric Department
Faculty of Medicine- Ain Shams University

3. Undifferntiated Gonad
Wolffian duct system
Mullerian duct system

5. GONADAL DEVELOPMENT
INTERNAL GENITALIA
7-8
weeks

6. External Genitalia
Normal Abnormal
Intersex
Hypogenitalism

7. Intersex
True
Pseudo: Female
Male

8. True Hermaphroditism
Definition •
Types •
Chromosomal Pattern •

13. DDeeffeecctt ooff TTeessttiiccuullaarr DDiiffffeerreennttiiaattiioonn
Absent HY antigen
Target Tissue Resistance
Embryonic Testicular Regression Syndrome
Bilateral Anorchia

14. DDyysshhoorrmmoonnooggeenneessiiss

15. UUtteerriinnee HHeerrnniiaa SSyynnddrroommee

16. DDeeffeecctt ooff AAnnddrrooggeenn AAccttiioonn
Testicular Feminization
Alpha-Reductase Deficiency-5

19. ..PPaarrttiiaall TT..FF

20. ..PPaarrttiiaall TT..FF

21. ..PPaarrttiiaall TT..FF

22. αα RReedduuccttaassee DDeeffiicciieennccyy--55

23. αα RReedduuccttaassee DDeeffiicciieennccyy--55

24. DDSSDD TTEEAAMM
Multidisciplinary
Endocrine
Genetics
Urology
Psychology/Psychiatry
Religious counseling
Gynecologist

25. SSEEXX AASSSSIIGGNNMMEENNTT
Actual Anatomy
Available surgical intervention
Functionl Endocrinology
Chromosomal Pattern
Non functioning female better than non
functioning male

27. Prader Willi Syndrome

28. PPuurree XXXX GGoonnaaddaall DDyyssggeenneessiiss

32. Thank You