1. Dr. Md. Jakir Hossain Bhuiyan
(Sohel)Resident PhaseâA
Dr MD AB QUIYUM
Resident,HBS,BSMMU
ABDOMINAL WALL DEFECTS
Welcome
2. OBJECTIVES
ď¨ Anatomy of abdominal wall in short
ď¨ What are the types of abdominal wall defects
ď¨ Embryology of different abdominal wall defects
ď¨ Diagnosis and management of different abdominal
wall defects
3. Borders of the Abdomen
⢠Superior:
Costal cartilages 7-12.
Xiphoid process:
Level of 10th cartilage = L3
⢠Inferior:
Pubic bone and iliac crest =Level of L4.
⢠Umbilicus:
Level of IV disc L3-4
4. Abdominal Quadrants
ďFormed by two intersecting lines:
Intersect at umbilicus.
ďQuadrants:
Upper left.
Upper right.
Lower left.
Lower right.
5. ABDOMINAL REGIONS
Divided into 9 regions by two pairs of planes:
âVertical Planes:
Left and right lateral planes
= midclavicular planes
âHorizontal Planes:
Transpyloric plane: tip 9 th CC
Intertubercular plane:Through tubercles of iliac
crests.
6. Fascia
⢠Superficial:Camperâs fascia Continuous with
fascia over thorax and thigh Fatty layer.
⢠Deep Superficial:Scarpaâs fascia
-Membranous layer:Continues into perineum
as:Superficial perineal fascia = Colleâs fascia.
⢠Deep: Thin layer covering abdominal muscles.
7. Muscle LayersMuscle Layers
ďGeneral Characteristics:
-Three large flat sheets connecting rib cage to
hip bone.
-Muscular posteriorly and laterally.
-Aponeurotic anteriorly and medially.
9. Arterial Supply
Above the Umbilicus:
âPIA 10-11.âSubcostal arteryâLA 1-4.
âMAâSuperior epigastric arteries.
âInferior epigastric arteries.
Below the Umbilicus:
â3s
10. Venous Drainage
⢠Superficial veins are paired with arteries.
⢠Above the umbilicus:
Drain into the azygos venous system.
⢠Below the umbilicus:
Drain into the femoral system (via great
saphenous).
11. OMPHALOCOELE
âAnterior abdominal wall defect at the base of
the umbilical cord with herniation of the
umbilical contents
Small omphalocoele 1:5000
Large omphalocoele 1:10000
Male to female ratio 1:1
Pacific Islanders have low risk for omphalocoele
12. Embryology of Omphalocele
⢠Failure of the midgut to return to abdomen by
the 10th
week of gestation
(Somatic layers of cephalic, caudal, and lateral
folds join to close abdominal wall)
14. Clinical Findings
⢠Covered clinical defect
of the umbilical ring
⢠Defect may vary from 2-
10 cm
⢠Sac is composed of
amnion, Whartonâs jelly
and peritoneum
⢠Associate ẽ
BA,IA,TTF,SD,VIF,CL
15. Clinical Findings
⢠50% have
accompanying liver,
spleen, testes/ovary
⢠>50% have associated
defects
⢠Location:
â Epigastric
â Central
â Hypogastric
⢠Cord attachment is on
the sac
17. GASTROSCHISISGASTROSCHISIS
ďDefect of the anterior abdominal wall just
lateral to the umbilicus
ď1:20,000-30,000
ďSex ratio 1:1
ď10-15% have associated anomalies
ď40% are premature/SGA
18. Embryology of Gastroschisis
ďAbnormal involution of right umbilical vein
ďRupture of a small omphalocoele
ďFailure of migration and fusion of the lateral folds of
the embryonic disc on the 3rd
-4th
week of gestation
ďLateral folds form
-Lateral abdominal wall
-Future umbilical ring
19. Clinical Findings
⢠Defect to the right of an
intact UC allowing extrusion
of abdominal content
⢠Opening â 5 cm
⢠No covering sac
38. Omphalocoele Gastroschisis
Incidence 1:6,000-10,000 1:20,000-30,000
Delivery Vaginal or CS CS
Covering Sac Present Absent
Size of Defect Small or large Small
Cord Location Onto the sac On abdominal wall
Bowel Normal Edematous, matted
39. Omphalocoele Gastroschisis
Other Organs Liver often out Rare
Prematurity 10-20% 50-60%
IUGR Less common Common
NEC If sac is ruptured 18%
Associated
Anomalies
>50% 10-15%
Treatment Often primary Often staged
Prognosis 20%-70% 70-90%
40. UMBILICAL HERNIA
⢠Defect in linea alba,
subcutaneous tissue
and skin covering the
protruding bowel
⢠Frequent in premature
infants
41. Pathophysiology
â In intrauterine life, there is a small opening
in the abdominal muscles that allows the UC
to pass through, connecting mother to baby.
â After birth, this opening in the abdominal
muscles closes.
âSometimes, these muscles do not meet and
grow together completely,
42. Clinical findings
⢠Bulge or swelling in the belly button area
⢠May become more noticeable when the baby
cries.
⢠May become smaller or disappear when the
baby is quiet
⢠Usually get smaller or go back into the
abdomen when gently pushes on the bulge
⢠Sometimes incarcerated hernia
43. MANAGEMENT
âMany umbilical hernias close spontaneously by
ages 3 to 4.
âIf closure does not occur by this time, surgical
repair is usually advised
âIn younger children, if there is an episode of
incarceration or if the hernia is very large, surgical
repair may be recommended.
44. PRUNE BELLY SYNDROME
(AMDS,CAAM, EBS,OS,FS & TS)
A group of birth defects that deal with three main
issues-
â˘Thin, flaccid abdominal wall
â˘Dilation of bladder, ureter and renal collecting
system
â˘UDT
â˘1:30,000-50,000
â˘95% are male
45. EMBRYOLOGY
⢠Myotomal cells from somites form ventral
and dorsal group migrating cells called
hypomeres
⢠If for some reasons hypomeric group does
not migrate,proliferate or differenciate
within the Abdominal resons
46. ⢠âLittle Buddhaâ appearance
⢠Constipation
⢠Delay in sitting and walking
⢠Difficulties coughing
⢠Difficulties in micturation
CLINICAL SYMPTOMS
47. BLADDER EXTROPHY
⢠Defective enfolding of
caudal folds
⢠3.3 in 100,000 births
⢠Associated with prolapsed
vagina or rectum,
epispadias, bifid clitoris or
penis
48. BLADDER EXTROPHY
âSpectrum of severity
-Small defect can result in epispadias
-large defect can result in exposure of
posterior bladder wall
âExposed bladder mucosa is edematous and
friable
49. EMBRYOLOGY
⢠It is partial form of spectrum of failure of
abdominal and pelvic fusions in the 1st
month
of embryogenesis
⢠It occurs as a result of defective migration of
genital tubercle primodii to the clocal
membrane and so malformation of the genital
tubercle at about 5th
week of gestation
50. MANAGEMENT
âMoist, fine-mesh gauze or vaseline gauze to cover
exposed bladder
âAntibiotics
âRenal ultrasound
âTransfer infant to surgical center
-Want surgical correction by 48-72 hours of life
-Sacroiliac joints are still pliable and the pelvis can be
âmoldedâ to allow better approximation of the pubic
rami
âIVP of limited utility b/c of poor concentrating ability
of neonatal kidney
51. MANAGEMENT
âTurn-in of the bladder to preserve bladder
function
âSymphysis pubis is approximated
Iliac osteotomies arenât necessary if ârepair
is within 48 HOL (bones are still pliable
from circulating maternal estrogens)
âEpispadiac urethra is reconstructed later
52. Cloacal Exstrophy
âVery rare: 1 in 200,000 births
âSporadic occurrence
âComplex of GI and GU anomalies:
-Imperforate anus
-Exstrophy of the bladder
-Omphalocele
-Vesicointestinal fistula
-Frequently prolapse of bowel thru the
fistula on bladder mucosa
53. EMBRYOLOGY
⢠Abnormal over development of the clocal
membrane which prevents medial
migration of the mesenchymal tissue and
proper lower abdominal wall development
54. MANAGEMENT
âCover exposed mucosa (vaseline/saline gauze)
and/or plastic wrap to minimize heat loss
âGender assignment / diagnosis
-Karyotype / FISH
-Controversial regarding assignment
âNG suction to relieve partial intestinal
obstruction.
-Stool frequently excreted through a vesico-
intestinal fistula that is often partially
obstructed
55. Cloacal Exstrophy - Operative
âSurvival 80% - mortality due to sepsis and
bowel obstruction
âPrompt surgery to separate fecal and urinary
streams
âBladder can be closed during initial procedure
if baby stable
âSubsequent procedures to reduce the number
of stomas and create genitalia
56. COMPLICATIONS
Multiple Long term problems:
Psychosocial / Gender Identification
Recurrent UTIs
Bowel/Bladder Incontinence
Sexual function in later life