11. Background
CrP is slow- growing & benign tumor.
Histologically benign epithelial tumor arising from squamous rests along
involuted hypophyseal-Rathke duct.
2 Types: Adamentinomatous & Papillary
6-9% of all Ped intracranial tumors.
Location: Suprasellar (75%), Supra & intrasellar ( 21%), Intrasellar (4%).
Age: Peak at 8-12 y.
Imaging findings: Cystic supracellar mass with calcification & enhancement
of a mural nodule of cyst wall. Displacement of chiasm.
90% are cystic; 90% have calcification; 90% enhancement cyst wall
Treatment: surgical & radiation therapy.
Prognosis: 64-96% overall 10 years survival
20% recurrence rate if <5cm
80% recurrence rate if> 5cm
Can recur up to 30 years after resection.