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Brugada Syndrome: Genetic Cardiac Sodium Channel Abnormality
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Overview of Brugada syndrome, including signs and symptoms, EKG findings, and treatment.
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Brugada Syndrome: Genetic Cardiac Sodium Channel Abnormality
1.
BRUGADA SYNDROME A
Brief Overview
2.
3.
Hereditary-60% of Brugada
patients have a family history of SCD
4.
5.
6.
Arrhythmias frequently occur
during sleep
7.
8.
First described at
NASPE meeting in 1991
9.
Review of literature
estimates that Brugada causes 4-12% of unexpected sudden deaths worldwide -Plus up to 50% of SCD in patients with normal hearts
10.
11.
Predominantly male
12.
13.
14.
15.
16.
AAD in Pts
with Normal EKG
17.
18.
19.
20.
Editor's Notes
Polymorphic VT
SE Asia- problem has been know for decades. In Thailand, it is called Lai Tai (death during sleep)
May be a higher percentage due to unfamiliarity with disease- “you see only what you look for- you recognize only what you know”
Causes of EKG variance
Confirms diagnosis of Brugada syndrome, and pt can be treated accordingly.
Hopefully, more and more will be discovered about this condition, so we can identify the patients at risk and get them the treatment they need.
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