Focuses on Epilepsy Management for poeple wth Tuberous Sclerosis. Includes information on: - Status Epilepticus - Epilepsy Management - First Aid Principles - Seizure Management Planning

2. Advances in Tuberous Sclerosis: From Pathway to Therapy Medical and Family Conference 3 – 4 November 2007 Sydney Children’s Hospital Randwick For more information: www.atss.org.au

3. I want to show you how it feels to have a seizure Hannah Age 9 157-6/05

7. “ Epilepsy is the most common serious neurological disorder affecting an estimated 50 million people worldwide” (WHO) Epilepsy

10. 36% 14% 7% 23% 6% 3% 8% 3% Seizure types Seizure Types

11. Seizure Classification Generalized Seizure involves whole brain & consciousness is affected Complex Altered awareness and behaviour Tonic Clonic “ grand-mal” or convulsion Atonic / Tonic “ drop attack” Myoclonic Sudden muscle jerks Absence “ petit mal” or staring fit Partial Seizure activity starts in one area of the brain Simple Retains awareness

12. Secondary generalization (spreading from one area to the whole brain) Complex Altered awareness and behaviour Partial Seizure activity starts in one area of the brain Simple Retains awareness Seizure Classification

13. Tonic Clonic “ grand-mal” or convulsion Atonic / Tonic “ drop attack” Myoclonic Sudden muscle jerks Absence “ petit mal” or staring fit Generalized Seizure involves whole brain & consciousness is affected Seizure Classification

15. Status Epilepticus “ Any seizure lasting for a duration of at least 30 minutes or longer from which a person does not regain consciousness” Appleton and Gibbs 1998

16. Convulsive Status Epilepticus Easily recognised medical emergency requiring aggressive treatment

17. Non-convulsive Status Epilepticus Subtle, under recognised, not considered to be life threatening Walker 2004

18. Non-convulsive Status Epilepticus Simple partial status epilepticus Complex partial status epilepticus Absence status epilepticus Generalised myoclonic status

35. Emergency medications are used for the control of seizures that may occur in clusters, prolonged seizures or status epilepticus Taking control – Emergency Medication Training

36. Taking control – Emergency Medication Training Indications Medical order Epilepsy awareness Training in administration Organisation require medication policy First Aid Certificate

40. This is me having a seizure in the classroom. All these things are happening around me and I’m not registering. I’m off in my own little world Amanda 15yrs 156-6/05

41. 1300 37 45 37

42. Advances in Tuberous Sclerosis: From Pathway to Therapy Medical and Family Conference 3 – 4 November 2007 Sydney Children’s Hospital Randwick For more information: www.atss.org.au